A cure for traffic jams: small molecule chaperones in the endoplasmic reticulum (Q35915766)

11 August 2017

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title

A cure for traffic jams: small molecule chaperones in the endoplasmic reticulum (English)

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11 August 2017

endoplasmic reticulum

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molecular chaperones

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author name string

Karin Römisch

series ordinal

1

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11 August 2017

1 November 2004

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11 August 2017

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11 August 2017

5

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11 August 2017

815-820

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11 August 2017

11

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Quality control in the endoplasmic reticulum protein factory

11 August 2017

1 reference

https://api.crossref.org/works/10.1111%2FJ.1600-0854.2004.00231.X

Protein dislocation from the endoplasmic reticulum--pulling out the suspect

21 January 2018

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Getting newly synthesized proteins into shape.

21 January 2018

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Repression of ribosome and tRNA synthesis in secretion-defective cells is signaled by a novel branch of the cell integrity pathway.

21 January 2018

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Effects of macromolecular crowding on protein folding and aggregation

21 January 2018

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Alpha1-antitrypsin deficiency. 4: Molecular pathophysiology

21 January 2018

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Roles of CHOP/GADD153 in endoplasmic reticulum stress

21 January 2018

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Traffic jam: a compendium of human diseases that affect intracellular transport processes

21 January 2018

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Traffic jams II: an update of diseases of intracellular transport

21 January 2018

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Processing of mutant cystic fibrosis transmembrane conductance regulator is temperature-sensitive

21 January 2018

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Intracellular retention of mutant retinoschisin is the pathological mechanism underlying X-linked retinoschisis

21 January 2018

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Pharmacological chaperones rescue cell-surface expression and function of misfolded V2 vasopressin receptor mutants

21 January 2018

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Therapeutic approaches to repair defects in deltaF508 CFTR folding and cellular targeting.

21 January 2018

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A contradictory treatment for lysosomal storage disorders: inhibitors enhance mutant enzyme activity

21 January 2018

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Aberrant retention of tyrosinase in the endoplasmic reticulum mediates accelerated degradation of the enzyme and contributes to the dedifferentiated phenotype of amelanotic melanoma cells

21 January 2018

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Calcium-pump inhibitors induce functional surface expression of Delta F508-CFTR protein in cystic fibrosis epithelial cells

21 January 2018

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Curcumin, a major constituent of turmeric, corrects cystic fibrosis defects

21 January 2018

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Evidence of CFTR function in cystic fibrosis after systemic administration of 4-phenylbutyrate

21 January 2018

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Evidence against the rescue of defective DeltaF508-CFTR cellular processing by curcumin in cell culture and mouse models.

21 January 2018

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The proteasome: a novel target for cancer chemotherapy

21 January 2018

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Protein degradation and protection against misfolded or damaged proteins

21 January 2018

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Folding proteins in fatal ways

21 January 2018

1 reference

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A naturally occurring protective system in urea-rich cells: mechanism of osmolyte protection of proteins against urea denaturation

21 January 2018

1 reference

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Yeast adapt to near-freezing temperatures by STRE/Msn2,4-dependent induction of trehalose synthesis and certain molecular chaperones

21 January 2018

1 reference

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Mechanism of protein stabilization by glycerol: preferential hydration in glycerol-water mixtures

21 January 2018

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The molecular mechanism of stabilization of proteins by TMAO and its ability to counteract the effects of urea

21 January 2018

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Trehalose-enzyme interactions result in structure stabilization and activity inhibition. The role of viscosity

21 January 2018

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Estimation of excess solvation numbers of water and cosolvents from preferential interaction and volumetric experiments.

21 January 2018

1 reference

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Preparation of extracts from higher eukaryotes

21 January 2018

1 reference

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Structural control of endoplasmic reticulum-associated degradation: effect of chemical chaperones on 3-hydroxy-3-methylglutaryl-CoA reductase

21 January 2018

1 reference

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Defective aquaporin-2 trafficking in nephrogenic diabetes insipidus and correction by chemical chaperones

21 January 2018

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Chemical chaperones mediate increased secretion of mutant alpha 1-antitrypsin (alpha 1-AT) Z: A potential pharmacological strategy for prevention of liver injury and emphysema in alpha 1-AT deficiency

21 January 2018

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Pharmacological chaperones: a new twist on receptor folding.

21 January 2018

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Pharmacological chaperones: potential treatment for conformational diseases.

21 January 2018

1 reference

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Major histocompatibility class I folding, assembly, and degradation: a paradigm for two-stage quality control in the endoplasmic reticulum

21 January 2018

1 reference

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Complexity in the secretory pathway: the assembly and secretion of apolipoprotein B-containing lipoproteins

21 January 2018

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Improvement in cardiac function in the cardiac variant of Fabry's disease with galactose-infusion therapy

21 January 2018

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The unfolded protein response: no longer just a special teams player

21 January 2018

1 reference

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Signaling the unfolded protein response from the endoplasmic reticulum.

21 January 2018

1 reference

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DeltaF508-CFTR causes constitutive NF-kappaB activation through an ER-overload response in cystic fibrosis lungs

21 January 2018

1 reference

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Activation of endoplasmic reticulum-specific stress responses associated with the conformational disease Z alpha 1-antitrypsin deficiency.

21 January 2018

1 reference

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The mechanism of Z alpha 1-antitrypsin accumulation in the liver

21 January 2018

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Familial dementia caused by polymerization of mutant neuroserpin

21 January 2018

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Do molecular chaperones have to be proteins?

21 January 2018

1 reference

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Molecular chaperones in the yeast endoplasmic reticulum maintain the solubility of proteins for retrotranslocation and degradation

21 January 2018

1 reference

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6-mer peptide selectively anneals to a pathogenic serpin conformation and blocks polymerization. Implications for the prevention of Z alpha(1)-antitrypsin-related cirrhosis

21 January 2018

1 reference

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Mutants of neuroserpin that cause dementia accumulate as polymers within the endoplasmic reticulum

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1600-0854.2004.00231.X

Regulation of protein secretion through controlled aggregation in the endoplasmic reticulum

21 January 2018

1 reference

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Correction of Defective Protein Kinesis of Human P-glycoprotein Mutants by Substrates and Modulators

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1600-0854.2004.00231.X

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1600-0854.2004.00231.X

10.1111/J.1600-0854.2004.00231.X

21 January 2018

Identifiers

DOI

1 reference

11 August 2017

1 reference

PubMed ID

15479447