State of the art and the dark side of amyotrophic lateral sclerosis. (Q37871837)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21540991%20AND%20SRC:MED&resulttype=core&format=json

30 January 2020

editorial

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title

State of the art and the dark side of amyotrophic lateral sclerosis (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21540991%20AND%20SRC:MED&resulttype=core&format=json

amyotrophic lateral sclerosis

30 January 2020

main subject

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author

Antonio Musarò

series ordinal

1

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https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21540991%20AND%20SRC:MED&resulttype=core&format=json

30 January 2020

author name string

Antonio Musarò

series ordinal

1

1 reference

24 August 2017

1 May 2010

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21540991%20AND%20SRC:MED&resulttype=core&format=json

World journal of biological chemistry

30 January 2020

published in

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30 January 2020

volume

1

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30 January 2020

issue

5

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30 January 2020

page(s)

62-68

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https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21540991%20AND%20SRC:MED&resulttype=core&format=json

MicroRNA pathways in neural development and plasticity.

30 January 2020

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Hyperactive intracellular calcium signaling associated with localized mitochondrial defects in skeletal muscle of an animal model of amyotrophic lateral sclerosis

6 September 2017

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Mutations in FUS, an RNA processing protein, cause familial amyotrophic lateral sclerosis type 6

6 September 2017

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6 September 2017

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Subcutaneous IGF-1 is not beneficial in 2-year ALS trial

6 September 2017

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Different regulation of wild-type and mutant Cu,Zn superoxide dismutase localization in mammalian mitochondria

6 September 2017

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Combining growth factor and stem cell therapy for amyotrophic lateral sclerosis

6 September 2017

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MicroRNAs flex their muscles

6 September 2017

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Selective association of misfolded ALS-linked mutant SOD1 with the cytoplasmic face of mitochondria.

6 September 2017

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Oxidized/misfolded superoxide dismutase-1: the cause of all amyotrophic lateral sclerosis?

6 September 2017

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ALS: astrocytes move in as deadly neighbors

6 September 2017

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Overexpression of CCS in G93A-SOD1 mice leads to accelerated neurological deficits with severe mitochondrial pathology

6 September 2017

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Amyotrophic lateral sclerosis: all roads lead to Rome

6 September 2017

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How do ALS-associated mutations in superoxide dismutase 1 promote aggregation of the protein?

6 September 2017

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Gene transfer demonstrates that muscle is not a primary target for non-cell-autonomous toxicity in familial amyotrophic lateral sclerosis

6 September 2017

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ALS: a disease of motor neurons and their nonneuronal neighbors

6 September 2017

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Molecular biology of amyotrophic lateral sclerosis: insights from genetics

6 September 2017

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Excitotoxicity and amyotrophic lateral sclerosis.

6 September 2017

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Mitochondria in amyotrophic lateral sclerosis: a trigger and a target

6 September 2017

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Failure of protein quality control in amyotrophic lateral sclerosis

6 September 2017

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Onset and progression in inherited ALS determined by motor neurons and microglia

6 September 2017

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6 September 2017

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6 September 2017

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Muscle expression of a local Igf-1 isoform protects motor neurons in an ALS mouse model

6 September 2017

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The Microprocessor complex mediates the genesis of microRNAs

6 September 2017

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A mutation in the vesicle-trafficking protein VAPB causes late-onset spinal muscular atrophy and amyotrophic lateral sclerosis

6 September 2017

1 reference

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Unraveling the mechanisms involved in motor neuron degeneration in ALS

6 September 2017

1 reference

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MicroRNAs: genomics, biogenesis, mechanism, and function

6 September 2017

1 reference

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ALS-associated mutant SOD1G93A causes mitochondrial vacuolation by expansion of the intermembrane space and by involvement of SOD1 aggregation and peroxisomes

6 September 2017

1 reference

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Update on the glutamatergic neurotransmitter system and the role of excitotoxicity in amyotrophic lateral sclerosis

6 September 2017

1 reference

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Role of mitochondria in oxidative stress and aging

6 September 2017

1 reference

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Mutant Cu, Zn superoxide dismutase that causes motoneuron degeneration is present in mitochondria in the CNS

6 September 2017

1 reference

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Localized Igf-1 transgene expression sustains hypertrophy and regeneration in senescent skeletal muscle

6 September 2017

1 reference

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Mutations in Cu/Zn superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis

6 September 2017

1 reference

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Motor neuron degeneration in mice that express a human Cu,Zn superoxide dismutase mutation

6 September 2017

1 reference

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Transgenic mice expressing an altered murine superoxide dismutase gene provide an animal model of amyotrophic lateral sclerosis

6 September 2017

1 reference

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Identification and characterization of a spinal muscular atrophy-determining gene

6 September 2017

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VAPB interacts with and modulates the activity of ATF6.

6 September 2017

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Muscle-derived neurotrophin-4 as an activity-dependent trophic signal for adult motor neurons

14 September 2017

1 reference

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MicroRNA-206 delays ALS progression and promotes regeneration of neuromuscular synapses in mice

28 September 2017

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Subcellular distribution of superoxide dismutases (SOD) in rat liver: Cu,Zn-SOD in mitochondria

23 June 2018

1 reference

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Development in the absence of skeletal muscle results in the sequential ablation of motor neurons from the spinal cord to the brain

23 June 2018

1 reference

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AAV-mediated expression of wild-type and ALS-linked mutant VAPB selectively triggers death of motoneurons through a Ca2+-dependent ER-associated pathway

23 June 2018

1 reference

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Amyotrophic lateral sclerosis mutant vesicle-associated membrane protein-associated protein-B transgenic mice develop TAR-DNA-binding protein-43 pathology.

1 September 2018

1 reference

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Local expression of mIgf-1 modulates ubiquitin, caspase and CDK5 expression in skeletal muscle of an ALS mouse model.

1 September 2018

1 reference

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Expanding the phenotypes of the Pro56Ser VAPB mutation: proximal SMA with dysautonomia.

1 September 2018

1 reference

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Wild-Type Nonneuronal Cells Extend Survival of SOD1 Mutant Motor Neurons in ALS Mice

1 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3083964

Retrograde viral delivery of IGF-1 prolongs survival in a mouse ALS model.

1 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3083964

Mutated human SOD1 causes dysfunction of oxidative phosphorylation in mitochondria of transgenic mice.

1 September 2018

1 reference

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SOD1 mutants linked to amyotrophic lateral sclerosis selectively inactivate a glial glutamate transporter

1 September 2018

1 reference

12 December 2020

Mitochondrial localization of mutant superoxide dismutase 1 triggers caspase-dependent cell death in a cellular model of familial amyotrophic lateral sclerosis

1 reference

12 December 2020

Amyotrophic lateral sclerosis

1 reference

12 December 2020

A VAPB mutant linked to amyotrophic lateral sclerosis generates a novel form of organized smooth endoplasmic reticulum

1 reference

12 December 2020

Neuron-specific expression of mutant superoxide dismutase is sufficient to induce amyotrophic lateral sclerosis in transgenic mice

1 reference

12 December 2020

Skeletal Muscle Is a Primary Target of SOD1G93A-Mediated Toxicity

1 reference

12 December 2020

Accumulation of SOD1 mutants in postnatal motoneurons does not cause motoneuron pathology or motoneuron disease

1 reference

12 December 2020

Identifiers

DOI

10.4331/WJBC.V1.I5.62

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21540991%20AND%20SRC:MED&resulttype=core&format=json

30 January 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21540991%20AND%20SRC:MED&resulttype=core&format=json

30 January 2020

PubMed publication ID

21540991

1 reference