RNA quality control and protein aggregates in amyotrophic lateral sclerosis: a review (Q38079170)

28 August 2017

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title

RNA quality control and protein aggregates in amyotrophic lateral sclerosis: a review (English)

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amyotrophic lateral sclerosis

28 August 2017

main subject

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quality control

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author name string

Ashok Verma

series ordinal

1

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28 August 2017

Rup Tandan

series ordinal

2

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28 August 2017

publication date

4 February 2013

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28 August 2017

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28 August 2017

volume

47

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28 August 2017

issue

3

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28 August 2017

page(s)

330-338

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Mutations in Cu/Zn superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis

28 August 2017

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Repeat expansion affects both transcription initiation and elongation in friedreich ataxia cells

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TLS (Translocated-in-Liposarcoma) Is a High-Affinity Interactor for Steroid, Thyroid Hormone, and Retinoid Receptors

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21 January 2018

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Mutant FUS proteins that cause amyotrophic lateral sclerosis incorporate into stress granules

21 January 2018

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21 January 2018

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Astrocytes expressing ALS-linked mutated SOD1 release factors selectively toxic to motor neurons

21 January 2018

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Superoxide dismutase 1 and tgSOD1 mouse spinal cord seed fibrils, suggesting a propagative cell death mechanism in amyotrophic lateral sclerosis

21 January 2018

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Astrocytes from familial and sporadic ALS patients are toxic to motor neurons

21 January 2018

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Interaction with polyglutamine aggregates reveals a Q/N-rich domain in TDP-43.

21 January 2018

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Prion-like disorders: blurring the divide between transmissibility and infectivity

21 January 2018

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A seeding reaction recapitulates intracellular formation of Sarkosyl-insoluble transactivation response element (TAR) DNA-binding protein-43 inclusions

21 January 2018

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ALS-associated fused in sarcoma (FUS) mutations disrupt Transportin-mediated nuclear import

21 January 2018

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A systematic survey identifies prions and illuminates sequence features of prionogenic proteins

21 January 2018

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FUS transgenic rats develop the phenotypes of amyotrophic lateral sclerosis and frontotemporal lobar degeneration

21 January 2018

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Knockdown of transactive response DNA-binding protein (TDP-43) downregulates histone deacetylase 6

21 January 2018

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A Drosophila model for TDP-43 proteinopathy

21 January 2018

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Gain and loss of function of ALS-related mutations of TARDBP (TDP-43) cause motor deficits in vivo

21 January 2018

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Loss of murine TDP-43 disrupts motor function and plays an essential role in embryogenesis

21 January 2018

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Neurotoxic effects of TDP-43 overexpression in C. elegans

21 January 2018

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TDP-43 transgenic mice develop spastic paralysis and neuronal inclusions characteristic of ALS and frontotemporal lobar degeneration

21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

1 reference

21 January 2018

Identifiers

DOI

10.1002/MUS.23673

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28 August 2017

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