Making sense of the spectrum of glomerular disease associated with complement dysregulation (Q38121480)

29 August 2017

title

Making sense of the spectrum of glomerular disease associated with complement dysregulation (English)

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29 August 2017

Sally Ann Johnson

1

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29 August 2017

Edwin K S Wong

series ordinal

2

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29 August 2017

C Mark Taylor

series ordinal

3

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29 August 2017

publication date

14 July 2013

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29 August 2017

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29 August 2017

volume

29

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29 August 2017

issue

10

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29 August 2017

page(s)

1883-1894

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Atypical hemolytic uremic syndrome

29 August 2017

cites work

1 reference

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Human C3 mutation reveals a mechanism of dense deposit disease pathogenesis and provides insights into complement activation and regulation

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Variations in the complement regulatory genes factor H (CFH) and factor H related 5 (CFHR5) are associated with membranoproliferative glomerulonephritis type II (dense deposit disease)

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Allelic variants of complement genes associated with dense deposit disease

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Deletion of Lys224 in regulatory domain 4 of Factor H reveals a novel pathomechanism for dense deposit disease (MPGN II)

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Causes of alternative pathway dysregulation in dense deposit disease

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Sensitive and specific assays for C3 nephritic factors clarify mechanisms underlying complement dysregulation

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21 January 2018

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Anti factor H autoantibodies block C-terminal recognition function of factor H in hemolytic uremic syndrome

21 January 2018

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21 January 2018

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Familial mesangio-capillary glomerulonephritis with initial presentation as haemolytic uraemic syndrome

21 January 2018

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Three kidneys, two diseases, one antibody?

21 January 2018

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Phenotypic expression of factor H mutations in patients with atypical hemolytic uremic syndrome.

21 January 2018

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Thrombotic microangiopathy mimicking membranoproliferative glomerulonephritis.

21 January 2018

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Translational mini-review series on complement factor H: renal diseases associated with complement factor H: novel insights from humans and animals.

21 January 2018

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Novel C3 mutation p.Lys65Gln in aHUS affects complement factor H binding

21 January 2018

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Complement factor H deficiency accelerates development of lupus nephritis

21 January 2018

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Terminal complement inhibitor eculizumab in atypical hemolytic-uremic syndrome

21 January 2018

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Eculizumab for dense deposit disease and C3 glomerulonephritis

21 January 2018

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Eculizumab for the Treatment of Dense-Deposit Disease

21 January 2018

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Eculizumab and Refractory Membranoproliferative Glomerulonephritis

21 January 2018

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Use of eculizumab for atypical haemolytic uraemic syndrome and C3 glomerulopathies

21 January 2018

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Glomeruli of Dense Deposit Disease contain components of the alternative and terminal complement pathway

21 January 2018

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https://api.crossref.org/works/10.1007%2FS00467-013-2559-8

Acquired and genetic complement abnormalities play a critical role in dense deposit disease and other C3 glomerulopathies

21 January 2018

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Haemolytic Uraemic Syndrome

21 January 2018

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12 December 2020

Heterogeneous pattern of renal disease associated with homozygous Factor H deficiency

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12 December 2020

C3 deposition glomerulopathy due to a functional factor H defect

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12 December 2020

Genetic studies into inherited and sporadic hemolytic uremic syndrome

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12 December 2020

The Complement Abnormalities of Lipodystrophy

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12 December 2020

Prognosis, treatment and outcome of childhood mesangiocapillary (membranoproliferative) glomerulonephritis

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12 December 2020

C3 nephritic factor and hypocomplementaemia in a clinically healthy individual

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12 December 2020

Anti-factor B autoantibody in dense deposit disease

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12 December 2020

Prognostic value of renal pathological findings in children with atypical hemolytic uremic syndrome.

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12 December 2020

Uncontrolled C3 activation causes membranoproliferative glomerulonephritis in mice deficient in complement factor H

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12 December 2020

Factor I is required for the development of membranoproliferative glomerulonephritis in factor H-deficient mice

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12 December 2020

10.1007/S00467-013-2559-8

Identifiers

DOI

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Dimensions Publication ID

29 August 2017

1040161737

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