Patient-Specific iPSC-Derived Endothelial Cells Uncover Pathways that Protect against Pulmonary Hypertension in BMPR2 Mutation Carriers (Q38778206)

19 July 2018

title

Patient-Specific iPSC-Derived Endothelial Cells Uncover Pathways that Protect against Pulmonary Hypertension in BMPR2 Mutation Carriers (English)

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19 July 2018

main subject

pulmonary hypertension

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19

Joseph C Wu

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19 July 2018

Jaecheol Lee

10

object named as

Jaecheol Lee

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19 July 2018

author name string

Mingxia Gu

1

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19 July 2018

Ning-Yi Shao

2

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Silin Sa

3

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Dan Li

4

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Vittavat Termglinchan

5

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Mohamed Ameen

6

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Ioannis Karakikes

7

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Gustavo Sosa

8

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Fabian Grubert

9

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Aiqin Cao

11

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Shalina Taylor

12

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Yu Ma

13

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Zhixin Zhao

14

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James Chappell

15

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Rizwan Hamid

16

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Eric D Austin

17

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Joseph D Gold

18

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Michael P Snyder

20

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Marlene Rabinovitch

21

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19 July 2018

language of work or name

English

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publication date

22 December 2016

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19 July 2018

published in

Cell Stem Cell

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19 July 2018

volume

20

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19 July 2018

issue

4

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19 July 2018

page(s)

490-504.e5

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19 July 2018

In Pulmonary Arterial Hypertension, Reduced BMPR2 Promotes Endothelial-to-Mesenchymal Transition via HMGA1 and Its Target Slug

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Gene expression in BMPR2 mutation carriers with and without evidence of pulmonary arterial hypertension suggests pathways relevant to disease penetrance

27 July 2018

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Endoglin germline mutation in a patient with hereditary haemorrhagic telangiectasia and dexfenfluramine associated pulmonary arterial hypertension

27 July 2018

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Molecular and functional analysis identifies ALK-1 as the predominant cause of pulmonary hypertension related to hereditary haemorrhagic telangiectasia

27 July 2018

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27 July 2018

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BMPR2 preserves mitochondrial function and DNA during reoxygenation to promote endothelial cell survival and reverse pulmonary hypertension

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31 August 2018

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31 August 2018

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31 August 2018

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31 August 2018

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31 August 2018

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PubMed

https://pubmed.ncbi.nlm.nih.gov/28017794

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

Identifiers

DOI

10.1016/J.STEM.2016.08.019

1 reference

19 July 2018

PMC publication ID

5500296

1 reference

19 July 2018

PubMed publication ID

28017794

1 reference

19 July 2018