Spontaneous generation of infectious nucleating amyloids in the transmissible and nontransmissible cerebral amyloidoses (Q40702826)

22 September 2017

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title

Spontaneous generation of infectious nucleating amyloids in the transmissible and nontransmissible cerebral amyloidoses (English)

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22 September 2017

D C Gajdusek

1

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22 September 2017

1 February 1994

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22 September 2017

Molecular Neurobiology

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22 September 2017

8

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22 September 2017

1

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22 September 2017

1-13

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https://scigraph.springernature.com/pub.10.1007/bf02778003

22 September 2017

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cites work

Prion protein mutation at codon 102 in an Italian family with Gerstmann-Sträussler-Scheinker syndrome

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A prion protein variant in a family with the telencephalic form of Gerstmann-Straussler-Scheinker syndrome

21 January 2018

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Atypical Creutzfeldt-Jakob disease in an American family with an insert mutation in the PRNP amyloid precursor gene

21 January 2018

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Codon 178 mutation in ethnically diverse Creutzfeldt-Jakob disease families

21 January 2018

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12 December 2020

An amber mutation of prion protein in Gerstmann-Sträussler syndrome with mutant PrP plaques

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12 December 2020

Mutation in codon 200 of scrapie amyloid precursor gene linked to Creutzfeldt-Jakob disease in Sephardic Jews of Libyan and non-Libyan origin

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12 December 2020

Phenotypic characteristics of familial Creutzfeldt-Jakob disease associated with the codon 178Asn PRNP mutation

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12 December 2020

Pro----leu change at position 102 of prion protein is the most common but not the sole mutation related to Gerstmann-Sträussler syndrome

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12 December 2020

Thermal stability and conformational transitions of scrapie amyloid (prion) protein correlate with infectivity

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12 December 2020

Familial Creutzfeldt-Jakob disease in Chile is associated with the codon 200 mutation of the PRNP amyloid precursor gene on chromosome 20.

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12 December 2020

Structure of prealbumin: secondary, tertiary and quaternary interactions determined by Fourier refinement at 1.8 A

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12 December 2020

The molecular genetics of familial Creutzfeldt-Jakob disease in France

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12 December 2020

Protein–DNA and protein–hormone interactions in prealbumin: a model of the thyroid hormone nuclear receptor?

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12 December 2020

Linkage of a prion protein missense variant to Gerstmann-Sträussler syndrome

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12 December 2020

EXPERIMENTAL AMYLOIDOSIS: STUDIES WITH A MODIFIED CASEIN METHOD, CASEIN HYDROLYSATE AND GELATIN

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12 December 2020

The phenotypic expression of different mutations in transmissible familial Creutzfeldt-Jakob disease.

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12 December 2020

The adoptive transfer of experimental mouse amyloidosis by intravenous injections of spleen cell extracts from casein-treated syngeneic donor mice

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12 December 2020

The new biology of spongiform encephalopathy: infectious amyloidoses with a genetic twist

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12 December 2020

Synthetic peptides corresponding to different mutated regions of the amyloid gene in familial Creutzfeldt-Jakob disease show enhanced in vitro formation of morphologically different amyloid fibrils

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12 December 2020

Pathogenetic mechanisms in protein-induced amyloidosis

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12 December 2020

Strjcture of human plasma prealbumin at 2-5 A resolution. A preliminary report on the polypeptide chain conformation, quaternary structure and thyroxine binding

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12 December 2020

New mutation in scrapie amyloid precursor gene (at codon 178) in Finnish Creutzfeldt-Jakob kindred

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12 December 2020

Experimental murine amyloidosis in x-irradiated recipients of spleen homogenates or serum from sensitized donors

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12 December 2020

Familial Creutzfeldt-Jakob disease in Finland: epidemiological, clinical, pathological and molecular genetic studies.

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12 December 2020

Insertion in prion protein gene in familial Creutzfeldt-Jakob disease

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12 December 2020

Familial Creutzfeldt-Jakob disease

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12 December 2020

Mutations in familial Creutzfeldt-Jakob disease and Gerstmann-Sträussler-Scheinker's syndrome

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12 December 2020

Mutation in codon 200 of scrapie amyloid protein gene in two clusters of Creutzfeldt-Jakob disease in Slovakia

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12 December 2020

Transmissible and non-transmissible amyloidoses: autocatalytic post-translational conversion of host precursor proteins to beta-pleated sheet configurations

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12 December 2020

An in-frame insertion in the prion protein gene in familial Creutzfeldt-Jakob disease

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12 December 2020

A new (two-repeat) octapeptide coding insert mutation in Creutzfeldt-Jakob disease

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12 December 2020

Codon 129 changes in the prion protein gene in Caucasians

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12 December 2020

Secondary structure of proteins associated in thin films

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12 December 2020

Enhancement of amyloid induction by amyloid fibril fragments in hamster.

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12 December 2020

Creutzfeldt-Jacob disease associated with the PRNP codon 200Lys mutation: an analysis of 45 families

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12 December 2020

Identical mutation in unrelated patients with Creutzfeldt-Jakob disease.

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12 December 2020

Creutzfeldt-Jakob disease and kuru patients lack a mutation consistently found in the Gerstmann-Sträussler-Scheinker syndrome

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12 December 2020

Mutant prion proteins in Gerstmann-Sträussler-Scheinker disease with neurofibrillary tangles

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12 December 2020

Focal accumulation of CJD in Slovakia: retrospective investigation of a new rural familial cluster

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12 December 2020

The constitution and genesis of amyloid.

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12 December 2020

The transmissible amyloidoses: Genetical control of spontaneous generation of infectious amyloid proteins by nucleation of configurational change in host precursors: Kuru-CJD-GSS-Scrapie-BSE

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12 December 2020

Molecular mass, biochemical composition, and physicochemical behavior of the infectious form of the scrapie precursor protein monomer

1 reference

12 December 2020

Structure of the chromosomal gene for human serum prealbumin

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12 December 2020

Linkage of the Indiana kindred of Gerstmann-Sträussler-Scheinker disease to the prion protein gene

1 reference

12 December 2020

Further characterization of amyloid-enhancing factor

1 reference

12 December 2020

An insert mutation in the chromosome 20 amyloid precursor gene in a Gerstmann-Sträussler-Scheinker family

1 reference

12 December 2020

Amyloid enhancing factor in hamster

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12 December 2020

An X-ray study of the subunit structure of prealbumin

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12 December 2020

Creutzfeldt-Jakob disease cosegregates with the codon 178Asn PRNP mutation in families of European origin

1 reference

12 December 2020

Identifiers

DOI

10.1007/BF02778003

1 reference

PubMed ID

8086124

Dimensions Publication ID

22 September 2017

0 references

1 reference

PubMed ID

8086124