Defective protein folding as a basis of human disease (Q40956747)

25 September 2017

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title

Defective protein folding as a basis of human disease (English)

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25 September 2017

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Thomas PJ

1

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PubMed ID

8578588

25 September 2017

Qu BH

series ordinal

2

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PubMed ID

8578588

25 September 2017

Pedersen PL

series ordinal

3

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25 September 2017

1 November 1995

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25 September 2017

4

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Trends in Biochemical Sciences

inferred from page(s)

published in

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25 September 2017

20

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25 September 2017

456-459

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25 September 2017

11

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Principles that govern the folding of protein chains

25 September 2017

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https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

Alternative packing arrangements in the hydrophobic core of λrepresser

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https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

Formation of a molten globule intermediate early in the kinetic folding pathway of apomyoglobin.

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https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

Protein folding in the cell

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https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

Peptide-binding specificity of the molecular chaperone BiP

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https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

Different conformations for the same polypeptide bound to chaperones DnaK and GroEL.

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https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

Protein folding in the cell: the role of molecular chaperones Hsp70 and Hsp60

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https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

ATP-induced protein-Hsp70 complex dissociation requires K+ but not ATP hydrolysis.

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https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

Chaperonin-mediated protein folding at the surface of groEL through a 'molten globule'-like intermediate

1 reference

https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

Calnexin: a membrane-bound chaperone of the endoplasmic reticulum

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https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

Occurrence and role of cis peptide bonds in protein structures

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https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis

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https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

Processing of mutant cystic fibrosis transmembrane conductance regulator is temperature-sensitive

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https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

Altered protein folding may be the molecular basis of most cases of cystic fibrosis

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https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

Conformational maturation of CFTR but not its mutant counterpart (delta F508) occurs in the endoplasmic reticulum and requires ATP

1 reference

https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

Fibrillin domain folding and calcium binding: significance to Marfan syndrome

1 reference

https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

Maple syrup urine disease in Mennonites. Evidence that the Y393N mutation in E1 alpha impedes assembly of the E1 component of branched-chain alpha-keto acid dehydrogenase complex

1 reference

https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

The LDL receptor locus in familial hypercholesterolemia: mutational analysis of a membrane protein

1 reference

https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

Collagen: molecular diversity in the body's protein scaffold

1 reference

https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

The alpha-helical to beta-strand transition in the amino-terminal fragment of the amyloid beta-peptide modulates amyloid formation

1 reference

https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

In pursuit of the molecular structure of amyloid plaque: new technology provides unexpected and critical information

1 reference

https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

Partial denaturation of transthyretin is sufficient for amyloid fibril formation in vitro

1 reference

https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

Co-overexpression of bacterial GroESL chaperonins partly overcomes non-productive folding and tetramer assembly of E. coli-expressed human medium-chain acyl-CoA dehydrogenase (MCAD) carrying the prevalent disease-causing K304E mutation.

1 reference

https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

Maturation and function of cystic fibrosis transmembrane conductance regulator variants bearing mutations in putative nucleotide-binding domains 1 and 2

1 reference

https://api.crossref.org/works/10.1016%2FS0968-0004%2800%2989100-8

7 January 2021

10.1016/S0968-0004(00)89100-8

Identifiers

DOI

1 reference

25 September 2017

1 reference

PubMed ID

8578588