Prion protein amyloidosis (Q41061823)

26 September 2017

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title

Prion protein amyloidosis (English)

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ORCID Public Data File 2021

26 September 2017

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Martin R. Farlow

8

object named as

Farlow MR

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26 September 2017

Ghetti B

1

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26 September 2017

Piccardo P

2

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26 September 2017

Frangione B

3

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26 September 2017

Bugiani O

4

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26 September 2017

Giaccone G

5

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26 September 2017

Young K

6

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26 September 2017

Prelli F

7

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26 September 2017

Dlouhy SR

9

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26 September 2017

Tagliavini F

10

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26 September 2017

1 April 1996

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26 September 2017

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26 September 2017

6

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26 September 2017

2

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26 September 2017

127-145

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Gerstmann-Sträussler syndrome--a variant type: amyloid plaques and Alzheimer's neurofibrillary tangles in cerebral cortex.

26 September 2017

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Spongiform encephalopathy transmitted experimentally from Creutzfeldt-Jakob and familial Gerstmann-Sträussler-Scheinker diseases.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Normal development and behaviour of mice lacking the neuronal cell-surface PrP protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Mice devoid of PrP are resistant to scrapie

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Secondary structure analysis of the scrapie-associated protein PrP 27-30 in water by infrared spectroscopy

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Truncated forms of the human prion protein in normal brain and in prion diseases.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Prion protein is necessary for normal synaptic function.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Linkage of the Indiana kindred of Gerstmann-Sträussler-Scheinker disease to the prion protein gene

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Pro----leu change at position 102 of prion protein is the most common but not the sole mutation related to Gerstmann-Sträussler syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Gerstmann-Sträussler-Scheinker disease. I. Extending the clinical spectrum.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Neurotoxicity of a prion protein fragment.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

A neurotoxic prion protein fragment induces rat astroglial proliferation and hypertrophy.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Predicted alpha-helical regions of the prion protein when synthesized as peptides form amyloid

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Vascular variant of prion protein cerebral amyloidosis with tau-positive neurofibrillary tangles: the phenotype of the stop codon 145 mutation in PRNP.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Neurofibrillary tangles of the Indiana kindred of Gerstmann-Sträussler-Scheinker disease share antigenic determinants with those of Alzheimer disease.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Prion protein preamyloid and amyloid deposits in Gerstmann-Sträussler-Scheinker disease, Indiana kindred

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Fatal familial insomnia and familial Creutzfeldt-Jakob disease: disease phenotype determined by a DNA polymorphism

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Processing of a cellular prion protein: identification of N- and C-terminal cleavage sites.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Molecular pathology of scrapie-associated fibril protein (PrP) in mouse brain affected by the ME7 strain of scrapie

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Linkage of a prion protein missense variant to Gerstmann-Sträussler syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

A prion protein variant in a family with the telencephalic form of Gerstmann-Straussler-Scheinker syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Mutant prion proteins in Gerstmann-Sträussler-Scheinker disease with neurofibrillary tangles

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Serial transmission in rodents of neurodegeneration from transgenic mice expressing mutant prion protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Proposed three-dimensional structure for the cellular prion protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

N-terminal sequence of prion protein is also integrated into kuru plaques in patients with Gerstmann-Sträussler syndrome.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

An amber mutation of prion protein in Gerstmann-Sträussler syndrome with mutant PrP plaques

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Novel missense variants of prion protein in Creutzfeldt-Jakob disease or Gerstmann-Sträussler syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Cell-free formation of protease-resistant prion protein.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Sulfated glycans stimulate endocytosis of the cellular isoform of the prion protein, PrPC, in cultured cells.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Human prion protein cDNA: molecular cloning, chromosomal mapping, and biological implications

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Immortality of cell cultures derived from brains of mice and hamsters infected with Creutzfeldt-Jakob disease agent

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Creutzfeldt-Jakob disease virus isolations from the Gerstmann-Sträussler syndrome with an analysis of the various forms of amyloid plaque deposition in the virus-induced spongiform encephalopathies

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Prion disease (PrP-A117V) presenting with ataxia instead of dementia

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Fatal familial insomnia and familial Creutzfeldt-Jakob disease: different prion proteins determined by a DNA polymorphism

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Familial dementia with PrP-positive amyloid plaques: a variant of Gerstmann-Sträussler syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

A cellular gene encodes scrapie PrP 27-30 protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Conversion of alpha-helices into beta-sheets features in the formation of the scrapie prion proteins

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Novel proteinaceous infectious particles cause scrapie

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Scrapie prions aggregate to form amyloid-like birefringent rods

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Molecular biology of prion diseases

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Genetic and infectious prion diseases

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Synthetic peptides homologous to prion protein residues 106-147 form amyloid-like fibrils in vitro

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

A68 is a component of paired helical filaments of Gerstmann-Sträussler-Scheinker disease, Indiana kindred.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Synthesis and trafficking of prion proteins in cultured cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Immunochemical, molecular genetic, and transmission studies on a case of Gerstmann-Straussler-Scheinker syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

Prion propagation in mice expressing human and chimeric PrP transgenes implicates the interaction of cellular PrP with another protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

A missense mutation at codon 105 with codon 129 polymorphism of the prion protein gene in a new variant of Gerstmann-Sträussler-Scheinker disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1750-3639.1996.TB00796.X

10.1111/J.1750-3639.1996.TB00796.X

21 January 2018

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DOI

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26 September 2017

1 reference