Partial restoration of defective chloride conductance in DeltaF508 CF mice by trimethylamine oxide (Q43638688)

25 November 2017

title

Partial restoration of defective chloride conductance in DeltaF508 CF mice by trimethylamine oxide (English)

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25 November 2017

3

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25 November 2017

Fischer H

1

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25 November 2017

Fukuda N

2

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25 November 2017

Illek B

4

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25 November 2017

Sartori C

5

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25 November 2017

Matthay MA

6

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25 November 2017

publication date

1 July 2001

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American Journal of Physiology - Lung Cellular and Molecular Physiology

25 November 2017

published in

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25 November 2017

volume

281

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25 November 2017

issue

1

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25 November 2017

page(s)

L52-7

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Development of substituted Benzo[c]quinolizinium compounds as novel activators of the cystic fibrosis chloride channel.

25 November 2017

cites work

1 reference

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Chemical chaperones correct the mutant phenotype of the delta F508 cystic fibrosis transmembrane conductance regulator protein

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Molecular chaperones and the centrosome. A role for HSP 73 in centrosomal repair following heat shock treatment

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Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis

21 January 2018

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Immediate early gene and HSP70 expression in hyperosmotic stress in MDCK cells

21 January 2018

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Ion-transporting activity in the murine colonic epithelium of normal animals and animals with cystic fibrosis

21 January 2018

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Chloride Conductance Expressed by ΔF508 and Other Mutant CFTRs In Xenopus Oocytes

21 January 2018

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Mechanism of protein stabilization by glycerol: preferential hydration in glycerol-water mixtures

21 January 2018

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Thermodynamic and kinetic examination of protein stabilization by glycerol

21 January 2018

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Maturation and function of cystic fibrosis transmembrane conductance regulator variants bearing mutations in putative nucleotide-binding domains 1 and 2

21 January 2018

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Intestinal physiology and pathology in gene-targeted mouse models of cystic fibrosis

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Anomalies in ion transport in CF mouse tracheal epithelium

21 January 2018

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Hyperabsorption of Na+ and raised Ca(2+)-mediated Cl- secretion in nasal epithelia of CF mice.

21 January 2018

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Delta F508-CFTR channels: kinetics, activation by forskolin, and potentiation by xanthines

21 January 2018

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Alternate stimulation of apical CFTR by genistein in epithelia

21 January 2018

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cAMP and genistein stimulate HCO3- conductance through CFTR in human airway epithelia

21 January 2018

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Defective function of the cystic fibrosis-causing missense mutation G551D is recovered by genistein

21 January 2018

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Expression of normal and cystic fibrosis phenotypes by continuous airway epithelial cell lines

21 January 2018

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Multiple proteolytic systems, including the proteasome, contribute to CFTR processing.

21 January 2018

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Efficiency of gene transfer for restoration of normal airway epithelial function in cystic fibrosis

21 January 2018

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Correction of the apical membrane chloride permeability defect in polarized cystic fibrosis airway epithelia following retroviral-mediated gene transfer

21 January 2018

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Mechanism of glibenclamide inhibition of cystic fibrosis transmembrane conductance regulator Cl- channels expressed in a murine cell line

21 January 2018

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An animal model for cystic fibrosis made by gene targeting

21 January 2018

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Degradation of CFTR by the ubiquitin-proteasome pathway

21 January 2018

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Influence of molecular and chemical chaperones on protein folding

21 January 2018

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A mouse model for the delta F508 allele of cystic fibrosis.

21 January 2018

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Altered chloride ion channel kinetics associated with the ΔF508 cystic fibrosis mutation

21 January 2018

1 reference

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10.1152/AJPLUNG.2001.281.1.L52

21 January 2018

Identifiers

DOI

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