C1q enhances cone photoreceptor survival in a mouse model of autosomal recessive retinitis pigmentosa (Q35603676)

9 August 2017

title

C1q enhances cone photoreceptor survival in a mouse model of autosomal recessive retinitis pigmentosa (English)

1 reference

9 August 2017

main subject

photoreceptor protein

0 references

7

Marina Botto

0 references

author name string

Marian M Humphries

1

1 reference

9 August 2017

Paul F Kenna

2

1 reference

9 August 2017

Matthew Campbell

3

1 reference

9 August 2017

Lawrence C S Tam

4

1 reference

9 August 2017

Anh T H Nguyen

5

1 reference

9 August 2017

G Jane Farrar

6

1 reference

9 August 2017

Marina Botto

7

1 reference

9 August 2017

Anna Sophia Kiang

8

1 reference

9 August 2017

Peter Humphries

9

1 reference

9 August 2017

publication date

24 August 2011

1 reference

European Journal of Human Genetics

9 August 2017

published in

1 reference

9 August 2017

volume

20

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9 August 2017

issue

1

1 reference

9 August 2017

page(s)

64-68

1 reference

Gene therapy rescues cone structure and function in the 3-month-old rd12 mouse: a model for midcourse RPE65 leber congenital amaurosis

9 August 2017

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12 July 2018

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Gene therapy with a promoter targeting both rods and cones rescues retinal degeneration caused by AIPL1 mutations

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Stimulation of the insulin/mTOR pathway delays cone death in a mouse model of retinitis pigmentosa

12 July 2018

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12 July 2018

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Mitochondrial DNA polymorphism A4917G is independently associated with age-related macular degeneration

12 July 2018

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12 July 2018

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12 July 2018

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C3 R102G polymorphism increases risk of age-related macular degeneration

12 July 2018

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12 July 2018

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12 July 2018

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12 July 2018

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12 July 2018

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12 July 2018

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12 July 2018

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12 July 2018

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12 July 2018

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12 July 2018

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12 July 2018

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12 July 2018

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12 July 2018

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12 July 2018

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12 July 2018

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12 July 2018

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12 July 2018

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12 July 2018

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25 September 2018

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Gene replacement therapy rescues photoreceptor degeneration in a murine model of Leber congenital amaurosis lacking RPGRIP.

25 September 2018

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Prolonged recovery of retinal structure/function after gene therapy in an Rs1h-deficient mouse model of x-linked juvenile retinoschisis

25 September 2018

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Toward a gene therapy for dominant disease: validation of an RNA interference-based mutation-independent approach

25 September 2018

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Clinical S-cone ERG recording with a commercial hand-held full-field stimulator

25 September 2018

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Long-term preservation of retinal function in the RCS rat model of retinitis pigmentosa following lentivirus-mediated gene therapy

25 September 2018

1 reference

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AAV-Mediated gene transfer slows photoreceptor loss in the RCS rat model of retinitis pigmentosa

25 September 2018

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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3234518

Intraocular gene delivery of ciliary neurotrophic factor results in significant loss of retinal function in normal mice and in the Prph2Rd2/Rd2 model of retinal degeneration

25 September 2018

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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3234518

The role of apoptosis in age-related macular degeneration

25 September 2018

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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3234518

Comparative structural and functional analysis of photoreceptor neurons of Rho-/- mice reveal increased survival on C57BL/6J in comparison to 129Sv genetic background

25 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3234518

Gene therapy restores vision in a canine model of childhood blindness

25 September 2018

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Standard for clinical electroretinography (2004 update).

25 September 2018

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Crossref

https://api.crossref.org/works/10.1038%2FEJHG.2011.151

Homozygous C1q deficiency causes glomerulonephritis associated with multiple apoptotic bodies

21 January 2018

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Crossref

https://api.crossref.org/works/10.1038%2FEJHG.2011.151

The globular heads of C1q specifically recognize surface blebs of apoptotic vascular endothelial cells

21 January 2018

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12 December 2020

Direct binding of C1q to apoptotic cells and cell blebs induces complement activation

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12 December 2020

Retinopathy induced in mice by targeted disruption of the rhodopsin gene

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12 December 2020

The electroretinogram of the rhodopsin knockout mouse

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12 December 2020

Identifiers

DOI

10.1038/EJHG.2011.151

1 reference

9 August 2017

1 reference

9 August 2017

1 reference