Huntingtin aggregate-associated axonal degeneration is an early pathological event in Huntington's disease mice. (Q45304186)

11 December 2017

Huntingtin aggregate-associated axonal degeneration is an early pathological event in Huntington's disease mice (English)

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12 May 2020

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H Li

1

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12 May 2020

S H Li

2

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Z X Yu

3

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P Shelbourne

4

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X J Li

5

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language of work or name

English

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publication date

1 November 2001

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11 December 2017

Journal of Neuroscience

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12 May 2020

volume

21

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issue

21

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12 May 2020

page(s)

8473-8481

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Selective sparing of a class of striatal neurons in Huntington's disease

12 May 2020

cites work

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12 December 2020

Increased apoptosis of Huntington disease lymphoblasts associated with repeat length-dependent mitochondrial depolarization

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12 December 2020

Intranuclear inclusions and neuritic aggregates in transgenic mice expressing a mutant N-terminal fragment of huntingtin

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12 December 2020

Motor disorder in Huntington's disease begins as a dysfunction in error feedback control.

1 reference

12 December 2020

Suppression of polyglutamine-mediated neurodegeneration in Drosophila by the molecular chaperone HSP70.

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12 December 2020

Mitochondrial dysfunction and free radical damage in the Huntington R6/2 transgenic mouse.

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12 December 2020

Axonal transport of N-terminal huntingtin suggests early pathology of corticostriatal projections in Huntington disease

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12 December 2020

Differential loss of striatal projection neurons in Huntington disease

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12 December 2020

Huntingtin acts in the nucleus to induce apoptosis but death does not correlate with the formation of intranuclear inclusions.

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12 December 2020

Amino-terminal fragments of mutant huntingtin show selective accumulation in striatal neurons and synaptic toxicity

1 reference

12 December 2020

Acute and chronic neuropathies: new aspects of Guillain-Barré syndrome and chronic inflammatory demyelinating polyneuropathy, an overview and an update

1 reference

12 December 2020

Axonal pathology in multiple sclerosis: relationship to neurologic disability

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12 December 2020

MRI demonstration of Wallerian degeneration in various intracranial lesions and its clinical implications.

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12 December 2020

Myelinated axon undergoes complete demyelination in the panencephalopathic--but it is merely subjected to the Wallerian degeneration in the polioencephalopathic type of transmissible spongiform encephalopathies

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12 December 2020

Preferential loss of striato-external pallidal projection neurons in presymptomatic Huntington's disease

1 reference

12 December 2020

Ultrastructural localization and progressive formation of neuropil aggregates in Huntington's disease transgenic mice

1 reference

12 December 2020

Magnetic resonance spectroscopy: imaging axonal damage in MS.

1 reference

12 December 2020

Genetic suppression of polyglutamine toxicity in Drosophila

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12 December 2020

Interference by huntingtin and atrophin-1 with cbp-mediated transcription leading to cellular toxicity

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12 December 2020

Exon 1 of the HD gene with an expanded CAG repeat is sufficient to cause a progressive neurological phenotype in transgenic mice

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12 December 2020

Abnormalities of striatal projection neurons and N-methyl-D-aspartate receptors in presymptomatic Huntington's disease

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12 December 2020

Nuclear and neuropil aggregates in Huntington's disease: relationship to neuropathology.

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12 December 2020

Huntingtin expression stimulates endosomal-lysosomal activity, endosome tubulation, and autophagy.

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12 December 2020

Formation of neuronal intranuclear inclusions underlies the neurological dysfunction in mice transgenic for the HD mutation

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12 December 2020

Expression of huntingtin-associated protein-1 in neuronal cells implicates a role in neuritic growth

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12 December 2020

Altered brain neurotransmitter receptors in transgenic mice expressing a portion of an abnormal human huntington disease gene

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12 December 2020

Severe early-onset polyneuropathy in insulin-dependent diabetes mellitus. A clinical and pathological study

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12 December 2020

Cellular defects and altered gene expression in PC12 cells stably expressing mutant huntingtin

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12 December 2020

Behavioural abnormalities and selective neuronal loss in HD transgenic mice expressing mutated full-length HD cDNA.

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12 December 2020

Impaired synaptic plasticity in mice carrying the Huntington's disease mutation

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12 December 2020

A YAC mouse model for Huntington's disease with full-length mutant huntingtin, cytoplasmic toxicity, and selective striatal neurodegeneration.

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12 December 2020

Oxidative damage and metabolic dysfunction in Huntington's disease: selective vulnerability of the basal ganglia.

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12 December 2020

Long glutamine tracts cause nuclear localization of a novel form of huntingtin in medium spiny striatal neurons in HdhQ92 and HdhQ111 knock-in mice

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12 December 2020

Mitochondrial involvement in Parkinson's disease, Huntington's disease, hereditary spastic paraplegia and Friedreich's ataxia

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12 December 2020

Neuropathological classification of Huntington's disease

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12 December 2020

Neurotransmitters and neuromodulators in the basal ganglia

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12 December 2020

Ataxin-1 nuclear localization and aggregation: role in polyglutamine-induced disease in SCA1 transgenic mice.

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12 December 2020

Dramatic mutation instability in HD mouse striatum: does polyglutamine load contribute to cell-specific vulnerability in Huntington's disease?

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12 December 2020

Caspase-8 is required for cell death induced by expanded polyglutamine repeats.

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12 December 2020

A Huntington's disease CAG expansion at the murine Hdh locus is unstable and associated with behavioural abnormalities in mice

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12 December 2020

Preferential loss of preproenkephalin versus preprotachykinin neurons from the striatum of Huntington's disease patients

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12 December 2020

Evidence for degenerative and regenerative changes in neostriatal spiny neurons in Huntington's disease

1 reference

12 December 2020

Aggregation of huntingtin in neuronal intranuclear inclusions and dystrophic neurites in brain

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12 December 2020

Dissection of autophagosome formation using Apg5-deficient mouse embryonic stem cells

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12 December 2020

Energetics in the pathogenesis of neurodegenerative diseases

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12 December 2020

Enhanced sensitivity to N-methyl-D-aspartate receptor activation in transgenic and knockin mouse models of Huntington's disease

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12 December 2020

Studies on the mechanisms of autophagy: formation of the autophagic vacuole

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12 December 2020

Decreased expression of striatal signaling genes in a mouse model of Huntington's disease

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12 December 2020

Abnormal synaptic plasticity and impaired spatial cognition in mice transgenic for exon 1 of the human Huntington's disease mutation.

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12 December 2020

Huntington aggregates may not predict neuronal death in Huntington's disease

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12 December 2020

10.1523/JNEUROSCI.21-21-08473.2001

Identifiers

DOI

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https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=PMCID:PMC6762783&resulttype=core&format=json

12 May 2020

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https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=PMCID:PMC6762783&resulttype=core&format=json

12 May 2020

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