Receptor-mediated and bulk-phase endocytosis cause macrophage and cholesterol accumulation in Niemann-Pick C disease (Q47598679)

4 February 2018

title

Receptor-mediated and bulk-phase endocytosis cause macrophage and cholesterol accumulation in Niemann-Pick C disease (English)

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4 February 2018

Niemann–Pick disease, type C

main subject

macrophage

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1 reference

Benny Liu

1

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4 February 2018

Chonglun Xie

2

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4 February 2018

James A Richardson

3

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4 February 2018

Stephen D Turley

4

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4 February 2018

John M Dietschy

5

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4 February 2018

publication date

2 May 2007

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4 February 2018

Journal of Lipid Research

published in

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4 February 2018

volume

48

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4 February 2018

issue

8

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4 February 2018

page(s)

1710-1723

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4 February 2018

Functional activities of hepatic lipoprotein receptors

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NPC2, the protein deficient in Niemann-Pick C2 disease, consists of multiple glycoforms that bind a variety of sterols

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21 January 2018

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21 January 2018

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Endosomal accumulation of Toll-like receptor 4 causes constitutive secretion of cytokines and activation of signal transducers and activators of transcription in Niemann-Pick disease type C (NPC) fibroblasts: a potential basis for glial cell activat

21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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Selective neurodegeneration, without neurofibrillary tangles, in a mouse model of Niemann-Pick C disease

21 January 2018

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Type-C Niemann-Pick disease: low density lipoprotein uptake is associated with premature cholesterol accumulation in the Golgi complex and excessive cholesterol storage in lysosomes

21 January 2018

1 reference

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10.1194/JLR.M700125-JLR200

21 January 2018

Identifiers

DOI

1 reference

4 February 2018

PubMed ID

17476031

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4 February 2018