Altered postnatal maturation of electrical properties in spinal motoneurons in a mouse model of amyotrophic lateral sclerosis. (Q51871496)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21486770%20AND%20SRC:MED&resulttype=core&format=json

28 January 2020

title

Altered postnatal maturation of electrical properties in spinal motoneurons in a mouse model of amyotrophic lateral sclerosis (English)

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amyotrophic lateral sclerosis

28 January 2020

main subject

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electrical properties

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author

Teepu Siddique

4

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28 January 2020

author name string

K A Quinlan

1

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28 January 2020

J E Schuster

2

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28 January 2020

R Fu

3

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28 January 2020

C J Heckman

5

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28 January 2020

language of work or name

English

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publication date

28 February 2011

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28 January 2020

published in

Journal of Physiology

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28 January 2020

volume

589

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28 January 2020

issue

Pt 9

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28 January 2020

page(s)

2245-2260

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Increased levels of p70S6 phosphorylation in the G93A mouse model of Amyotrophic Lateral Sclerosis and in valine-exposed cortical neurons in culture.

28 January 2020

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Early detection of denervated muscle fibers in hindlimb muscles after sciatic nerve transection in wild type mice and in the G93A mouse model of amyotrophic lateral sclerosis.

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Cortical hyperexcitability may precede the onset of familial amyotrophic lateral sclerosis

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25 August 2018

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25 August 2018

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25 August 2018

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Serotonin facilitates a persistent calcium current in motoneurons of rats with and without chronic spinal cord injury

25 August 2018

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The role of excitotoxicity in the pathogenesis of amyotrophic lateral sclerosis.

25 August 2018

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25 August 2018

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Altered excitability of motor neurons in a transgenic mouse model of familial amyotrophic lateral sclerosis.

25 August 2018

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alpha-Amino-3-hydroxy-5-methyl-isoxazole-4-propionate receptors in spinal cord motor neurons are altered in transgenic mice overexpressing human Cu,Zn superoxide dismutase (Gly93-->Ala) mutation.

25 August 2018

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Hyperexcitability of cultured spinal motoneurons from presymptomatic ALS mice.

25 August 2018

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Persistent sodium and calcium currents cause plateau potentials in motoneurons of chronic spinal rats

25 August 2018

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Functional specialization of the axon initial segment by isoform-specific sodium channel targeting.

25 August 2018

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5-HT2 receptors promote plateau potentials in turtle spinal motoneurons by facilitating an L-type calcium current.

25 August 2018

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Mechanisms causing plateau potentials in spinal motoneurones.

25 August 2018

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Plateau potentials in sacrocaudal motoneurons of chronic spinal rats, recorded in vitro

25 August 2018

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25 August 2018

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25 August 2018

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25 August 2018

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25 August 2018

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25 August 2018

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25 August 2018

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25 August 2018

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25 August 2018

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The Golgi apparatus of spinal cord motor neurons in transgenic mice expressing mutant Cu,Zn superoxide dismutase becomes fragmented in early, preclinical stages of the disease

25 August 2018

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Neuropathological changes in two lines of mice carrying a transgene for mutant human Cu,Zn SOD, and in mice overexpressing wild type human SOD: a model of familial amyotrophic lateral sclerosis (FALS).

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Preferential motor unit loss in the SOD1 G93A transgenic mouse model of amyotrophic lateral sclerosis

25 August 2018

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12 December 2020

Electrophysiological properties of two axonal sodium channels, Nav1.2 and Nav1.6, expressed in mouse spinal sensory neurones

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Changes during the postnatal development in physiological and anatomical characteristics of rat motoneurons studied in vitro

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Persistent inward currents in rat ventral horn neurones

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Riluzole inhibits the persistent sodium current in mammalian CNS neurons

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Intrinsic properties of lumbar motor neurones in the adult G127insTGGG superoxide dismutase-1 mutant mouse in vivo: evidence for increased persistent inward currents

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Properties of a persistent inward current in normal and TEA-injected motoneurons

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Activation patterns of embryonic chick hind limb muscles recorded in ovo and in an isolated spinal cord preparation

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Functional motor unit failure precedes neuromuscular degeneration in canine motor neuron disease

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Selective loss of alpha motoneurons innervating the medial gastrocnemius muscle in a mouse model of amyotrophic lateral sclerosis

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Massive mitochondrial degeneration in motor neurons triggers the onset of amyotrophic lateral sclerosis in mice expressing a mutant SOD1

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Early electrophysiological abnormalities in lumbar motoneurons in a transgenic mouse model of amyotrophic lateral sclerosis

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Time course of preferential motor unit loss in the SOD1 G93A mouse model of amyotrophic lateral sclerosis

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10.1113/JPHYSIOL.2010.200659

Identifiers

DOI

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21486770%20AND%20SRC:MED&resulttype=core&format=json

28 January 2020

PMC publication ID

3098701

0 references

1 reference