Misfolded CuZnSOD and amyotrophic lateral sclerosis (Q24683677)

amyotrophic lateral sclerosis

Europe PubMed Central

title

Misfolded CuZnSOD and amyotrophic lateral sclerosis (English)

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main subject

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author name string

Joan Selverstone Valentine

series ordinal

1

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P John Hart

series ordinal

2

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language of work or name

English

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publication date

1 April 2003

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published in

Proceedings of the National Academy of Sciences of the United States of America

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volume

100

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issue

7

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page(s)

3617-22

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cites work

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Fibrillar inclusions and motor neuron degeneration in transgenic mice expressing superoxide dismutase 1 with a disrupted copper-binding site

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Proteasomal-dependent aggregate reversal and absence of cell death in a conditional mouse model of Huntington's disease.

28 November 2018

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Mice lacking cytosolic copper/zinc superoxide dismutase display a distinctive motor axonopathy

28 November 2018

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Superoxide dismutase and neurofilament transgenic models of amyotrophic lateral sclerosis.

28 November 2018

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Mutant SOD1 causes motor neuron disease independent of copper chaperone-mediated copper loading

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12 December 2020

The metal binding properties of the zinc site of yeast copper-zinc superoxide dismutase: implications for amyotrophic lateral sclerosis

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Identification of oxidized histidine generated at the active site of Cu,Zn-superoxide dismutase exposed to H2O2. Selective generation of 2-oxo-histidine at the histidine 118

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12 December 2020

Cu/Zn superoxide dismutase-like immunoreactivity in Lewy body-like inclusions of sporadic amyotrophic lateral sclerosis

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12 December 2020

Prevention of mutant SOD1 motoneuron degeneration by copper chelatorsin vitro

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12 December 2020

Sporadic amyotrophic lateral sclerosis with dementia and Cu/Zn superoxide dismutase-positive Lewy body-like inclusions

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12 December 2020

Immunohistochemical study on superoxide dismutases in spinal cords from autopsied patients with amyotrophic lateral sclerosis

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12 December 2020

Transgenic animal models of familial amyotrophic lateral sclerosis

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12 December 2020

Superoxide-dependent peroxidase activity of H48Q: a superoxide dismutase variant associated with familial amyotrophic lateral sclerosis

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12 December 2020

Mutant superoxide dismutase-1-linked familial amyotrophic lateral sclerosis: molecular mechanisms of neuronal death and protection

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12 December 2020

Massive mitochondrial degeneration in motor neurons triggers the onset of amyotrophic lateral sclerosis in mice expressing a mutant SOD1

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12 December 2020

Protein oxidative damage in a transgenic mouse model of familial amyotrophic lateral sclerosis

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12 December 2020