Pathological mitochondrial copper overload in livers of Wilson's disease patients and related animal models. (Q38187164)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24517326%20AND%20SRC:MED&resulttype=core&format=json

7 March 2020

title

Pathological mitochondrial copper overload in livers of Wilson's disease patients and related animal models (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24517326%20AND%20SRC:MED&resulttype=core&format=json

7 March 2020

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24517326%20AND%20SRC:MED&resulttype=core&format=json

7 March 2020

author name string

Josef Lichtmannegger

series ordinal

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24517326%20AND%20SRC:MED&resulttype=core&format=json

7 March 2020

language of work or name

English

0 references

publication date

12 February 2014

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24517326%20AND%20SRC:MED&resulttype=core&format=json

Annals of the New York Academy of Sciences

7 March 2020

published in

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24517326%20AND%20SRC:MED&resulttype=core&format=json

7 March 2020

volume

1315

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24517326%20AND%20SRC:MED&resulttype=core&format=json

7 March 2020

page(s)

6-15

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24517326%20AND%20SRC:MED&resulttype=core&format=json

7 March 2020

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

The Wilson disease gene is a copper transporting ATPase with homology to the Menkes disease gene

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

The Wilson disease gene is a putative copper transporting P-type ATPase similar to the Menkes gene

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Isolation and characterization of a human liver cDNA as a candidate gene for Wilson disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Mechanisms for copper acquisition, distribution and regulation

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Inherited copper transport disorders: biochemical mechanisms, diagnosis, and treatment

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Wilson's disease: an update.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Evolving perspectives in Wilson disease: diagnosis, treatment and monitoring

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Diagnosis and treatment of Wilson disease: an update

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Coupling of phosphorylation to electron and hydrogen transfer by a chemi-osmotic type of mechanism

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

The cancer cell's "power plants" as promising therapeutic targets: an overview

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Yeast contain a non-proteinaceous pool of copper in the mitochondrial matrix.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

SOD1 and mitochondria in ALS: a dangerous liaison.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Mitochondrial involvement in genetically determined transition metal toxicity II. Copper toxicity

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Fundamental aspects of reactive oxygen species, or what's the matter with oxygen?

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

A mitochondrial paradigm of metabolic and degenerative diseases, aging, and cancer: a dawn for evolutionary medicine

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Human SCO2 is required for the synthesis of CO II and as a thiol-disulphide oxidoreductase for SCO1.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Copper trafficking to the mitochondrion and assembly of copper metalloenzymes

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Iron and copper in mitochondrial diseases

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Liver mitochondrial membrane crosslinking and destruction in a rat model of Wilson disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Mitochondrial matrix copper complex used in metallation of cytochrome oxidase and superoxide dismutase

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Metal Ion availability in mitochondria.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

The yeast mitochondrial proteome, a study of fermentative and respiratory growth

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Copper import into the mitochondrial matrix in Saccharomyces cerevisiae is mediated by Pic2, a mitochondrial carrier family protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Free radicals and antioxidants in normal physiological functions and human disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Free radicals, metals and antioxidants in oxidative stress-induced cancer

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Glutathionylation of mitochondrial proteins

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Undetectable intracellular free copper: the requirement of a copper chaperone for superoxide dismutase

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Affinity gradients drive copper to cellular destinations

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

TISSUE COPPER PROTEINS IN WILSON'S DISEASE. INTRACELLULAR DISTRIBUTION AND CHROMATOGRAPHIC FRACTIONATION.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Mitochondria, oxidative stress and cell death

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

The role of mitochondria in pharmacotoxicology: a reevaluation of an old, newly emerging topic.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Role of mitochondrial DNA in toxic responses to oxidative stress

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Mitochondrial DNA damage is more extensive and persists longer than nuclear DNA damage in human cells following oxidative stress

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Uptake and effects of copper in rat liver mitochondria

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

The mitochondrial permeability transition from in vitro artifact to disease target

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Calcium, mitochondria and reperfusion injury: a pore way to die.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Mitochondrial gateways to cancer

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Studies of copper ion-induced mitochondrial swelling in vitro

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

In vitro modulation of heavy metal-induced rat liver mitochondria dysfunction: a comparison of copper and mercury with cadmium.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

The puzzle posed by COMMD1, a newly discovered protein binding Cu(II).

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Cu(I)-glutathione complex: a potential source of superoxide radicals generation

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Cu2+ toxicity inhibition of mitochondrial dehydrogenases in vitro and in vivo

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Copper-dependent toxicity in SH-SY5Y neuroblastoma cells involves mitochondrial damage.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Animal models of copper-associated liver disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Systems biology approach to Wilson's disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Consequences of copper accumulation in the livers of the Atp7b-/- (Wilson disease gene) knockout mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Severe dysfunction of respiratory chain and cholesterol metabolism in Atp7b(-/-) mice as a model for Wilson disease.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Mitochondrial structure and function in the untreated Jackson toxic milk (tx-j) mouse, a model for Wilson disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

The LEC rat has a deletion in the copper transporting ATPase gene homologous to the Wilson disease gene

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Expression of the Wilson disease gene is deficient in the Long-Evans Cinnamon rat.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Spontaneous hepatic copper accumulation in Long-Evans Cinnamon rats with hereditary hepatitis. A model of Wilson's disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

A new strain of rat for functional analysis of PINA.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

How mitochondria produce reactive oxygen species

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Treatment of Wilson's disease: the historical background

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Brain metal accumulation in Wilson's disease.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Morphologic alterations produced by copper in neural tissues with consideration of the role of the metal in the pathogenesis of Wilson's disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Neuroinflammatory and behavioural changes in the Atp7B mutant mouse model of Wilson's disease.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Neurochemical and behavioral characteristics of toxic milk mice: an animal model of Wilson's disease.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

A semi-automated method for isolating functionally intact mitochondria from cultured cells and tissue biopsies

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

The treatment of Wilson's disease, a rare genetic disorder of copper metabolism

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FNYAS.12347

Intracellular localization of the Menkes and Wilson's disease proteins and their role in intracellular copper transport

21 January 2018

1 reference

5 June 2022

https://opencitations.net/index/coci/api/v1/citations/10.1046/J.1442-200X.1999.01090.X

Identifiers

DOI

10.1111/NYAS.12347

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24517326%20AND%20SRC:MED&resulttype=core&format=json

7 March 2020

1 reference