Ribosomal Stalk Protein Silencing Partially Corrects the ΔF508-CFTR Functional Expression Defect (Q28551966)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27168400%20AND%20SRC:MED&resulttype=core&format=json

4 April 2020

title

Ribosomal Stalk Protein Silencing Partially Corrects the ΔF508-CFTR Functional Expression Defect (English)

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4 April 2020

1

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4 April 2020

Kathryn E Oliver

2

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4 April 2020

Pirjo M Apaja

3

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4 April 2020

Doranda Perdomo

4

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4 April 2020

Aurélien Bidaud-Meynard

5

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4 April 2020

Sheng-Ting Lin

6

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4 April 2020

Mert Icyuz

8

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4 April 2020

John L Hartman

10

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4 April 2020

Gergely L Lukacs

11

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4 April 2020

9

Eric J Sorscher

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4 April 2020

author name string

Jingyu Guo

7

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4 April 2020

language of work or name

English

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publication date

11 May 2016

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4 April 2020

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4 April 2020

volume

14

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4 April 2020

issue

5

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4 April 2020

page(s)

e1002462

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Creative Commons Attribution 4.0 International

4 April 2020

copyright license

start time

11 May 2016

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April 2022 Public Data File from Crossref

copyright status

copyrighted

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describes a project that uses

ImageJ

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11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC4864299/fullTextXML

inferred from PubMed Central ID database lookup

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29 September 2017

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29 September 2017

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29 September 2017

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29 September 2017

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Mutational disruption of plasma membrane trafficking of Saccharomyces cerevisiae Yor1p, a homologue of mammalian multidrug resistance protein

29 September 2017

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Analysis of the localization of STE6/CFTR chimeras in a Saccharomyces cerevisiae model for the cystic fibrosis defect CFTR delta F508.

29 September 2017

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Identification of revertants for the cystic fibrosis delta F508 mutation using STE6-CFTR chimeras in yeast

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Ribosomal Acidic Phosphoproteins P1 and P2 Are Not Required for Cell Viability but Regulate the Pattern of Protein Expression in Saccharomyces cerevisiae

29 September 2017

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Conformational maturation of CFTR but not its mutant counterpart (delta F508) occurs in the endoplasmic reticulum and requires ATP

29 September 2017

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Cystic fibrosis: molecular biology and therapeutic implications

29 September 2017

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Molecular insights into the interaction of the ribosomal stalk protein with elongation factor 1α.

29 September 2017

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Quantitative proteomic profiling reveals differentially regulated proteins in cystic fibrosis cells

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4864299

Carboxy terminal modifications of the P0 protein reveal alternative mechanisms of nuclear ribosomal stalk assembly

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4864299

Efficient delivery of RNA interference oligonucleotides to polarized airway epithelia in vitro

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4864299

Correction of both NBD1 energetics and domain interface is required to restore ΔF508 CFTR folding and function

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4864299

The ribosome modulates nascent protein folding

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4864299

Use of primary cultures of human bronchial epithelial cells isolated from cystic fibrosis patients for the pre-clinical testing of CFTR modulators

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4864299

Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4864299

3 June 2018

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PBIO.1002462

Corrector VX-809 stabilizes the first transmembrane domain of CFTR.

21 January 2018

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PBIO.1002462

Silent substitutions predictably alter translation elongation rates and protein folding efficiencies

21 January 2018

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PBIO.1002462

Visualization of elongation factor Tu on the Escherichia coli ribosome.

21 January 2018

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PBIO.1002462

Lasker Basic Medical Research Award. SEC mutants and the secretory apparatus

21 January 2018

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PBIO.1002462

Structural and functional characterization of the amino terminal domain of the yeast ribosomal stalk P1 and P2 proteins.

21 January 2018

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PBIO.1002462

Synthetic genetic array analysis in Saccharomyces cerevisiae.

21 January 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4864299

In vivo cell-specific expression of the cystic fibrosis transmembrane conductance regulator

27 November 2018

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PBIO.1002462

Interaction of elongation factor eEF-2 with ribosomal P proteins

21 January 2018

1 reference

12 December 2020

New scenarios of protein folding can occur on the ribosome

1 reference

12 December 2020

Mislocalization of ΔF508 CFTR in cystic fibrosis sweat gland

1 reference

12 December 2020

Yeast ribosomal P0 protein has two separate binding sites for P1/P2 proteins

1 reference

12 December 2020

Modelling neurodegeneration in Saccharomyces cerevisiae: why cook with baker's yeast?

1 reference

12 December 2020

The delta F508 mutation decreases the stability of cystic fibrosis transmembrane conductance regulator in the plasma membrane. Determination of functional half-lives on transfected cells

1 reference

12 December 2020

Optimizing membrane-protein biogenesis through nonoptimal-codon usage

1 reference

12 December 2020

10.1371/JOURNAL.PBIO.1002462

Identifiers

DOI

2 references

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27168400%20AND%20SRC:MED&resulttype=core&format=json

4 April 2020

1 reference

2 references

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27168400%20AND%20SRC:MED&resulttype=core&format=json

4 April 2020

PubMed publication ID

27168400

2 references